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KMID : 0363219760140040389
Korean Journal of Dermatology
1976 Volume.14 No. 4 p.389 ~ p.393
Mucha-Habermann¢¥s Disease (Pityriasis Lichenoids et Varioliformis Acuta)
õËçµó¾/Choi, Young Chan
òÌûóßÂ/ðáð£Îú/Chin, Hong Sang/Cho, Chung Koo
Abstract
Mucha-Habermann disease is cutaneous disease of unknown etilogy and characterized. by a polymorphous eruption consisting of papulosquamous, hemorrhagic, ulceronecrotic lesion eventually into varioliform scars.
It is also classified into parapsoriasis group according to Broq with parapsoriasis. en guttata (pityriasis lichenoides chronica), parapsoriasis en plaques, parapsoriasis en lichenoides.
The 61-year-old male patient visited to Dermatologic Department of Severance Hospital due to sudden onset of generalized eruption. He presented pea to finger tip sized erythematous, silvery maculo-papulo-squamous eruptions on trunk, extremities and buttock, but didn¢¥t complain of any subjective symptoms except marked fatigue.
Skin biopsy was done on right forearm and was confirmed to pityriasis lichenoides et varioliformis acuta by histopathologic finding. The lesion was completely controlled by oral tetracycline 2.Ogm per daily for first 4 weeks and reduced dosage 1.Ogm per day for second 2 weeks.
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